Dyke-Davidoff-Masson Syndrome with crossed cerebellar atrophy

Dyke-Davidoff-Masson Syndrome (DDMS) is a rare neurological condition characterised clinically by recurrent seizures, facial asymmetry, hemiplegia and mental retardation likely due to foetal or early childhood cerebral insult. We describe the MRI findings of DDMS in 10-year-old male child. brain revealed right atrophy, ipsilateral thickening calvarium, lateral ventricular dilatation, hyper-pneumatisation frontal sinus, contralateral cerebellar atrophy which are consistent with DDMS.